Hess Jason, Lonergan Ian, Rozzelle Arlene A, Arneja Jugpal S
Section of Plastic Surgery, Children's Hospital of Michigan and Wayne State University, Detroit, Michigan 48201, USA.
J Craniofac Surg. 2008 Jul;19(4):1126-30. doi: 10.1097/SCS.0b013e31817636ae.
Apert syndrome is a congenital condition characterized by craniosynostosis, syndactyly, and maxillary hypoplasia. Previous authors have outlined the management of craniofacial and extremity anomalies associated with this syndrome; however, there is a paucity of literature regarding the treatment of the cutaneous manifestations of Apert syndrome. Axillary osmidrosis, a chronic skin condition characterized by an excessive, axillary malodor resulting from apocrine gland dysfunction, can be particularly severe in patients with Apert syndrome. Herein, we describe a pediatric patient with Apert syndrome and severe axillary osmidrosis managed by an arthroscopic shaver technique of axillary glandular debridement and aspiration.
Apert综合征是一种先天性疾病，其特征为颅缝早闭、并指（趾）畸形和上颌骨发育不全。既往作者已概述了与该综合征相关的颅面和肢体异常的处理方法；然而，关于Apert综合征皮肤表现治疗的文献却很匮乏。腋窝臭汗症是一种慢性皮肤疾病，其特征是由于顶泌汗腺功能障碍导致腋窝出现过度的恶臭，在Apert综合征患者中可能尤为严重。在此，我们描述了一名患有Apert综合征和严重腋窝臭汗症的儿科患者，采用关节镜下剃须刀技术进行腋窝腺体清创和抽吸治疗。
