Soden Jason S, Narkewicz Michael R, Haas Joel E, Sokol Ronald J
Pediatric Liver Center and Liver Transplantation Program, Department of Pediatrics, University of Colorado Denver School of Medicine, and The Children's Hospital, Aurora, CO 80045, USA.
J Pediatr. 2009 Feb;154(2):299-302. doi: 10.1016/j.jpeds.2008.08.048.
Hepatobiliary disease has been described in Bruton's x-linked agammaglobulinemia; however, veno-occlusive disease has not been reported in this setting. We report a case of end-stage liver disease in a patient with x-linked agammaglobulinemia who was found to have VOD and evidence of human herpes virus 7 infection in the explanted liver after transplantation.
在布鲁顿氏X连锁无丙种球蛋白血症中曾有肝胆疾病的描述;然而,在这种情况下尚未有肝静脉闭塞病的报道。我们报告了一例X连锁无丙种球蛋白血症患者的终末期肝病病例,该患者在移植后切除的肝脏中被发现患有肝静脉闭塞病且有人类疱疹病毒7感染的证据。