Garcia-Consuegra J, Barrio M I, Fonseca E, Rodriguez J I, Contreras F
Department of Paediatrics, La Paz Hospital, Madrid, Spain.
Eur J Pediatr. 1991 May;150(7):468-9. doi: 10.1007/BF01958423.
We report a 12-year-old girl with nodular skin lesions, fever, pancytopenia, coagulation defects and a fatal outcome within 4 months. Histopathology revealed proliferation of histiocytes with haemophagocytosis in skin, perivisceral fat and haemopoietic organs. The symptoms were most consistent with cytophagic histiocytic panniculitis.