Li Szu-Yuan, Jiang Jeng-Kai, Chang Yen-Hwa, Wu Te-Chang, Yang Wu-Chang, Ng Yee-Yung
Department of Medicine, Taipei Veterans General Hospital, Taipei, Taiwan, Republic of China.
J Chin Med Assoc. 2009 Mar;72(3):153-5. doi: 10.1016/S1726-4901(09)70042-5.
Patients with autosomal dominant polycystic kidney disease (ADPKD) usually have extrarenal manifestations. We report the case of a 53-year-old man with ADPKD who presented with a retroperitoneal abscess of the left side after undergoing bilateral nephrectomy for a cyst that had repeatedly bled for 1 year. The abscess recurred despite drainage with a pig-tail catheter and antibiotic treatment. Fistulography with injection of diluted contrast medium via the pig-tail catheter showed an accumulation of contrast medium in the descending colon, which indicated a fistula between the abscess and the descending colon. A portion of the descending colon was resected, and multiple diverticulitis with 1 perforation in the resected specimen was observed. The findings support a diagnosis of retroperitoneal abscess caused by a perforated diverticulum---an extrarenal manifestation of ADPKD.
常染色体显性多囊肾病(ADPKD)患者通常有肾外表现。我们报告一例53岁的ADPKD男性患者,其在因反复出血1年的囊肿行双侧肾切除术后出现左侧腹膜后脓肿。尽管通过猪尾导管引流并给予抗生素治疗,脓肿仍复发。经猪尾导管注入稀释造影剂进行瘘管造影显示造影剂在降结肠积聚,提示脓肿与降结肠之间存在瘘管。切除了部分降结肠,在切除标本中观察到多发憩室炎伴1处穿孔。这些发现支持由穿孔憩室引起的腹膜后脓肿的诊断——这是ADPKD的一种肾外表现。