Rocchietti March Massimiliano, De Palma Carmela, L'Angiocola Paolo Diego, Aliberti Giuseppe
UOC Medicina Interna, II Facoltà di Medicina e Chirurgia, Università La Sapienza, Azienda Ospedaliera Sant'Andrea, Roma.
Recenti Prog Med. 2008 Dec;99(12):602-5.
Pheochromocytomas are catecholamine-producing neuroendocrine tumors arising from chromaffine cells derived from the embryonic neural crest. They occur in 0.1-5.7% of patients with neurofibromatosis type 1 (von Recklinghausen's disease). We report the case of an adrenal pheochromocytoma in a patient with neurofibromatosis type 1.
嗜铬细胞瘤是起源于胚胎神经嵴衍生的嗜铬细胞的儿茶酚胺分泌性神经内分泌肿瘤。它们见于1型神经纤维瘤病(冯·雷克林豪森病)患者的0.1%至5.7%。我们报告1例1型神经纤维瘤病患者发生肾上腺嗜铬细胞瘤的病例。