Korać Petra, Peran Ivana, Skrtić Anita, Ajduković Radmila, Kristo Delfa Radić, Dominis Mara
Department of Clinical Pathology and Cytology, University Hospital Merkur, Zagreb, Croatia.
Pathol Int. 2009 May;59(5):354-8. doi: 10.1111/j.1440-1827.2009.02377.x.
Multiple myeloma (MM) is a clonal disorder of terminally differentiated B cells. In some cases the premalignant state is monoclonal gammopathy of undetermined significance (MGUS). Neoplastic plasma cells in both entities carry multiple and complex chromosomal abnormalities that make understanding of the disease development difficult. New insight into malignant mechanisms that underlie multiple myeloma may come from forkhead box P1 transcription factor (FOXP1) analysis in neoplastic plasma cells. FOXP1 is known to be important for B-cell maturation and differentiation and could play a significant role in plasma cell tumors. The purpose of the present study was therefore to analyze FOXP1 protein presence and FOXP1 gene abnormalities in 13 cases of MGUS and 60 cases of MM. It was found that FOXP1 protein was expressed in neoplastic plasma cells, unlike in their normal counterparts, and that additional FOXP1 gene copies could be found in both MGUS and MM. Based on FOXP1 presence in MM and its role in diffuse large B-cell lymphoma and extranodal marginal zone lymphoma of mucosa-associated lymphoid tissue, FOXP1 might play an important role in plasma cell neoplasm.
多发性骨髓瘤(MM)是一种终末分化B细胞的克隆性疾病。在某些情况下,癌前状态为意义未明的单克隆丙种球蛋白病(MGUS)。这两种疾病中的肿瘤性浆细胞都存在多种复杂的染色体异常,这使得了解疾病的发展变得困难。对多发性骨髓瘤潜在恶性机制的新见解可能来自对肿瘤性浆细胞中叉头框P1转录因子(FOXP1)的分析。已知FOXP1对B细胞成熟和分化很重要,并且可能在浆细胞瘤中发挥重要作用。因此,本研究的目的是分析13例MGUS和60例MM中FOXP1蛋白的存在情况以及FOXP1基因异常。研究发现,与正常浆细胞不同,肿瘤性浆细胞中表达FOXP1蛋白,并且在MGUS和MM中均可发现额外的FOXP1基因拷贝。基于FOXP1在MM中的存在及其在弥漫性大B细胞淋巴瘤和黏膜相关淋巴组织结外边缘区淋巴瘤中的作用,FOXP1可能在浆细胞肿瘤中发挥重要作用。