Farah-Klibi Faten, El Amine Olfa, Rammeh Soumaya, Ben Rejeb Majd, Ferchiou Malek, Kourda Jihène, Abdessalem Morched, Zaouche Abdeljalil, Ben Jilani Sarrah, Zermani Rachida
Laboratoire d'Anatomie et de Cytologie Pathologiques, Hôpital Charles Nicolle, Tunis, Tunisie.
Tunis Med. 2008 Oct;86(10):928-31.
Solid pseudopapillary tumors of the pancreas are extremely rare and mostly seen in young females. It is often diagnosed incidentally or during investigations of gastrointestinal complaints.
Report of a pediatric case of this tumor.
We report the case of a 15-year old teenager who presented with painful abdominal tumefaction. Imaging findings were a 12 cm solid and cystic mass originating from the tail of the pancreas. A distal pancreatectomy with splenectomy was performed. Pathologic examination concluded to solid pseudopapillary tumor. Evolution was favorable with no recurrence 18 months after surgery.
Histological examination confirms the diagnosis and allows, with the help of immunohistochemical study, to rule out some differential diagnoses such as pancreatoblastoma, acinar tumors and endocrine tumors. Prognosis of solid pseudopapillary tumors of the pancreas is excellent after radical resection and recurrences are rarely seen.
胰腺实性假乳头状肿瘤极为罕见,多见于年轻女性。通常在偶然情况下或在胃肠道不适检查期间被诊断出来。
报告该肿瘤的一例儿科病例。
我们报告一例15岁青少年病例,该患者出现腹部疼痛性肿块。影像学检查发现一个12厘米的实性和囊性肿块,起源于胰尾。进行了远端胰腺切除术加脾切除术。病理检查诊断为实性假乳头状肿瘤。术后18个月病情进展良好,无复发。
组织学检查可确诊,并借助免疫组化研究排除一些鉴别诊断,如胰腺母细胞瘤、腺泡肿瘤和内分泌肿瘤。胰腺实性假乳头状肿瘤根治性切除术后预后良好,很少复发。