Hematology 2 Unit, San Giovanni Battista Hospital and University, Turin, Italy.
Biol Blood Marrow Transplant. 2010 Jan;16(1):115-22. doi: 10.1016/j.bbmt.2009.09.011. Epub 2009 Sep 18.
Iron overload (IO) is a known adverse prognostic factor in patients who undergo allogeneic hematopoietic stem cell transplantation (HSCT) for thalassemia and appears to play a similar role in patients with other hematologic disorders. The estimation of IO is based primarily on serum ferritin level; however, many confounding factors can result in ferritin overestimation, especially in HSCT recipients. The aim of the present study was to quantify IO after HSCT using a superconducting quantum interference device (SQUID), and to evaluate the impact of IO on hepatic function and infections. In addition, the feasibility of iron depletion was investigated. A total of 102 consecutive allogeneic HSCT recipients admitted to our outpatient department between December 2005, and December 2007, were analyzed. Primary diagnosis included acute leukemia/myelodysplastic syndrome in 61% of cases. Assessment of IO after HSCT included serum ferritin; in those with hyperferritinemia (ferritin>1000 ng/mL), liver iron concentration (LIC) was evaluated by SQUID magnetic susceptometry. Iron removal therapy was offered to patients with moderate IO (LIC 1000-2000 microg Fe/g wet weight [ww]) or severe IO (LIC >2,000 microg Fe/g ww). Fifty-seven patients had a ferritin level <1000 ng/mL: the median time between HSCT and assessment of ferritin level was 1006 days (range, 93-5239 days), significantly different from the median time of 183 days (range, 78-2957 days) in the 45 patients with a ferritin level >1000 ng/mL. Out of 42 patients evaluated by SQUID, 29 had moderate to severe IO (median LIC value, 1493 microg Fe/g ww [range, 1030-3253]). In a multivariate analysis, a significant correlation was found between a ferritin level >1000 ng/mL and the presence of at least one abnormal liver function test (LFT) ORo=6.8; 95% CI=2.2-20.6). In addition, the rate of proven/probable invasive fungal disease was significantly higher in the patients with hyperferritinemia (13% vs 0%; P=.006). Nineteen of the 24 patients considered eligible for iron-depletion therapy underwent regular phlebotomy; 13 completed the program in a median of 287 days (range, 92-779 days), reaching the target of a ferritin level<500 ng/mL; LIC was significantly reduced (median, 1419 microg Fe/g ww to 625 microg Fe/g ww; P < .001) in 8 of the 9 patients who were revaluated by SQUID at the end of the iron-depletion program. In conclusion, the measurement of LIC obtained by SQUID documented the presence of moderate/severe IO in 69% of the patients with a high ferritin level. Our data showed that in HSCT recipients, high ferritin level is an independent risk factor for abnormal LFTs, and IO may be considered a potential risk factor for fungal infections. A phlebotomy program may be feasible in two-thirds of the patients who might benefit from iron depletion.
铁过载 (IO) 是接受同种异体造血干细胞移植 (HSCT) 治疗地中海贫血患者的已知不良预后因素,似乎在其他血液系统疾病患者中也发挥着类似的作用。IO 的评估主要基于血清铁蛋白水平;然而,许多混杂因素会导致铁蛋白高估,尤其是在 HSCT 受者中。本研究的目的是使用超导量子干涉装置 (SQUID) 定量评估 HSCT 后的 IO,并评估 IO 对肝功能和感染的影响。此外,还研究了铁耗竭的可行性。共分析了 2005 年 12 月至 2007 年 12 月期间在我院门诊就诊的 102 例连续接受同种异体 HSCT 的患者。主要诊断包括急性白血病/骨髓增生异常综合征占 61%。HSCT 后 IO 的评估包括血清铁蛋白;在铁蛋白升高的患者中(铁蛋白>1000ng/ml),采用 SQUID 磁强计评估肝铁浓度(LIC)。对中度 IO(LIC 1000-2000μg Fe/g 湿重 [ww])或重度 IO(LIC>2000μg Fe/g ww)的患者给予铁去除治疗。57 例患者铁蛋白水平<1000ng/ml:HSCT 与铁蛋白水平评估之间的中位时间为 1006 天(范围 93-5239 天),与铁蛋白水平>1000ng/ml 的 45 例患者的中位时间 183 天(范围 78-2957 天)显著不同。在 42 例接受 SQUID 评估的患者中,29 例存在中重度 IO(中位 LIC 值 1493μg Fe/g ww [范围 1030-3253])。在多变量分析中,铁蛋白水平>1000ng/ml 与至少一项异常肝功能试验(LFT)之间存在显著相关性(OR=6.8;95%CI=2.2-20.6)。此外,铁蛋白升高患者侵袭性真菌病的确诊/可能发生率显著更高(13%比 0%;P=.006)。24 例有资格进行铁耗竭治疗的患者中有 19 例接受了定期放血治疗;13 例在中位 287 天(范围 92-779 天)内完成了治疗方案,达到铁蛋白水平<500ng/ml 的目标;9 例患者中有 8 例在铁耗竭治疗方案结束时接受了 SQUID 重新评估,LIC 显著降低(中位值,从 1419μg Fe/g ww 降至 625μg Fe/g ww;P<.001)。总之,SQUID 测量的 LIC 显示,69%的高铁蛋白水平患者存在中重度 IO。我们的数据表明,在 HSCT 受者中,高铁蛋白水平是肝功能异常的独立危险因素,IO 可能是真菌感染的潜在危险因素。放血方案可能对三分之二的可能受益于铁耗竭的患者可行。
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