Wang Jingfu, Pei Guanghua, Yan Jie, Zhang Guangchao
Department of Pediatric Oncology, Key Laboratory of Cancer Prevention and Therapy of Tianjin, Tianjin Medical University Cancer Institute and Hospital, Tianjin, China.
J Pediatr Hematol Oncol. 2009 Dec;31(12):983-4. doi: 10.1097/MPH.0b013e3181bdbaf3.
A 4-month girl presenting with a giant mass in left adrenal region and multiple hepatic nodules was hospitalized. On the basis of computed tomography, ultrasound and epidemiology we preferred the diagnosis of a left adrenal neuroblastoma accompanied with multiple hepatic metastases preoperatively. But postoperative diagnosis was hemangiomatosis characterized by synchronous presence of a giant splenic hemangioma and multiple hepatic hemangiomas. We think that it is deservedly reported because of not only its rarity but also pitfalls of preoperative differential diagnosis and management principle.
一名4个月大的女童因左肾上腺区巨大肿块及多发肝结节入院。根据计算机断层扫描、超声检查及流行病学情况,我们术前倾向于诊断为左肾上腺神经母细胞瘤伴多发肝转移。但术后诊断为血管瘤病,其特征为同时存在巨大脾血管瘤和多发肝血管瘤。我们认为该病例值得报道,不仅因其罕见,还因其术前鉴别诊断的难点及处理原则。