Santos-Briz Angel, Cañueto Javier, Antúnez Patricia, Bravo Javier, García-Sanz Ramón, de Unamuno Pablo
Department of Pathology, Hospital Universitario de Salamanca, Salamanca, Spain.
Am J Dermatopathol. 2010 Feb;32(1):86-90. doi: 10.1097/DAD.0b013e3181b1c62f.
Amyloid elastosis is a rare form of cutaneous amyloidosis characterized histologically by the deposition of amyloid-coating elastic fibers of the skin. To date, only 4 cases have been reported, all of them in the setting of systemic amyloidosis. We present the first case of primary cutaneous localized amyloid elastosis.
淀粉样弹性组织变性是一种罕见的皮肤淀粉样变性,组织学特征为皮肤弹性纤维上有淀粉样物质沉积。迄今为止,仅报道过4例,均发生在系统性淀粉样变性背景下。我们报告首例原发性皮肤局限性淀粉样弹性组织变性。