1st Department of Cardiology, Poznań University of Medical Sciences, Długa 1/2, 61-848 Poznań, Poland.
Cardiol J. 2010;17(1):11-9.
The remarkable improvement in pediatric cardiosurgery observed over the last few decades has meant that many patients with congenital heart diseases have entered adult life. The growing population of adults with congenital heart defects (ACHD) requires specialized treatment. The team of specialists should consist of cardiologists experienced in congenital heart diseases, cardiosurgeons, obstetricians and anesthesiologists. The need for providing ACHD with appropriate healthcare remains largely unmet. The proper care of ACHD requires an excellent knowledge of defect residuals and post-operative sequel complications. The commonest clinical problems are arrhythmias, impulse formation and conduction disorders as well as heart failure with complicated pathophysiology. The medical management of these patients is mainly based on doctors' experience, since Evidence Based Medicine recommendations do not cover the above mentioned clinical issues. Cyanosis must be distinguished as another clinical problem for which treatment requires special knowledge. For many women with congenital heart diseases, pregnancy and delivery may be hazardous. To date, observations show that most patients with congenital heart diseases enjoy a full life.
过去几十年中，儿科心脏外科学取得了显著进步，许多患有先天性心脏病的患者已经进入成年期。患有先天性心脏病（ACHD）的成年人人数不断增加，这需要专门的治疗。专家团队应由经验丰富的心脏病专家、心脏外科医生、妇产科医生和麻醉师组成。为 ACHD 提供适当的医疗保健的需求在很大程度上仍未得到满足。对 ACHD 的适当护理需要对缺陷残余和术后并发症有极好的了解。最常见的临床问题是心律失常、冲动形成和传导障碍以及伴有复杂病理生理学的心力衰竭。这些患者的医疗管理主要基于医生的经验，因为循证医学建议并不涵盖上述临床问题。紫绀必须与另一个临床问题区分开来，因为治疗这种疾病需要特殊的知识。对于许多患有先天性心脏病的女性来说，怀孕和分娩可能是危险的。迄今为止，观察结果表明，大多数患有先天性心脏病的患者都能过上完整的生活。
