儿童特发性肺动脉高压。

Idiopathic pulmonary arterial hypertension in childhood.

机构信息

Great Ormond St Hospital for Children, University College Institute of Child Health, London, UK.

出版信息

Cardiol Rev. 2010 Mar-Apr;18(2):64-6. doi: 10.1097/CRD.0b013e3181ce03df.

PMID:20160530

Abstract

The introduction of new medicines to treat pulmonary vascular disease has renewed interest in the management of children with idiopathic pulmonary arterial hypertension. We now have a practical classification of pulmonary hypertension, improved diagnostic techniques, and internationally recognized diagnostic and management guidelines. In 2009 the UK Pulmonary Hypertension Service for Children reported survival figures for idiopathic pulmonary arterial hypertension of 85.6% at 1 year, 79.9% at 3 years, and 71.9% at 5 years. A good quality of life can be assured for many years.

摘要

新型药物的出现为治疗肺血管疾病带来了新的希望，也重新激起了人们对特发性肺动脉高压患儿治疗的兴趣。目前，我们已经拥有实用的肺动脉高压分类、改良的诊断技术以及国际认可的诊断和管理指南。2009 年，英国儿童肺动脉高压服务机构报告称特发性肺动脉高压患儿的 1 年生存率为 85.6%，3 年生存率为 79.9%，5 年生存率为 71.9%。许多患儿的生活质量在多年内都能得到保障。