De Franco A, Brizi M G, Barbaro B, Buffa V, Vecchioli A, Marano P
Istituto di Radiologia, Università Cattolica del Sacro Cuore, Roma.
Radiol Med. 1991 Apr;81(4):459-63.
From 1987 to 1989, 7 patients were diagnosed as having a primary lymphoma of the small bowel. The patients, 5 men and 2 women aged 14-66 years (average: 45), were studied by means of small bowel enema and CT. Using small bowel enema, our findings were: masses related to a loop, stenosis, mucosal patterns with thick, irregular, and nodular folds, and bowel walls thickening. In nearly all cases CT showed not only small bowel lesions but also mesenteric lymphadenopathy. Five of seven patients had lymphomas, 1 had IP-SID lymphoma (immunoproliferative small intestinal disease related lymphoma), and 1 had IPSID associated with a late prelymphomatous stage. The diagnosis of IPSID is very important in patients with malabsorption syndrome, which may or may not be related to alpha heavy chain disease, because IPSID may evolve into lymphoma but its prelymphomatous stage can be treated and cured. We have therefore reported the different features seen with enteroclysis and CT, comparing the results obtained in the various forms of lymphoma of the small bowel. The importance is stressed of an accurate diagnosis of IPSID forms, however uncommon in our Country.
1987年至1989年期间,7例患者被诊断为原发性小肠淋巴瘤。这些患者中,5名男性和2名女性,年龄在14至66岁之间(平均45岁),通过小肠灌肠和CT进行了研究。通过小肠灌肠,我们的发现如下:与肠袢相关的肿块、狭窄、黏膜形态表现为增厚、不规则和结节状褶皱,以及肠壁增厚。几乎在所有病例中,CT不仅显示了小肠病变,还显示了肠系膜淋巴结肿大。7例患者中有5例患有淋巴瘤,1例患有免疫增殖性小肠疾病相关淋巴瘤(IP-SID淋巴瘤),1例患有与淋巴瘤前期晚期相关的免疫增殖性小肠疾病(IPSID)。IPSID的诊断对于吸收不良综合征患者非常重要,该综合征可能与α重链病有关,也可能无关,因为IPSID可能会演变为淋巴瘤,但其淋巴瘤前期阶段可以得到治疗和治愈。因此,我们报告了小肠灌肠和CT所见的不同特征,比较了在各种小肠淋巴瘤形式中获得的结果。强调了准确诊断IPSID形式的重要性,尽管在我国这种情况并不常见。