Ertürk Cemil, Yarmpapuç Raci, Altay Mehmet Akif, Büyükbebeci Orhan, Ozsaraç Mehmet Coşkun
Faculty of Medicine, Department of Orthopaedic Surgery, Harran University Sanliurfa, Turkey.
J Pediatr Orthop B. 2010 Jul;19(4):348-52. doi: 10.1097/BPB.0b013e32833831fc.
Congenital fibrosarcoma is a rare, malignant, soft-tissue tumor in infants and the pediatric age group. The clinical behavior of congenital fibrosarcoma is more favorable, and metastatic spread is rare, but local recurrence is a common problem. The patient was a 1-year-old girl at the time of operation, and there was a giant mass in the posterior region of the right leg. A wide surgical excision was performed and histological findings showed the diagnosis of congenital fibrosarcoma. After one and a half years, femoral supracondylar amputation was performed because of the recurrence of the local tumor.
先天性纤维肉瘤是一种罕见的、恶性的软组织肿瘤,好发于婴儿及儿童年龄段。先天性纤维肉瘤的临床行为相对较好,转移扩散少见,但局部复发是常见问题。该患者手术时为1岁女童,右腿后部有一巨大肿块。进行了广泛的手术切除,组织学检查结果显示为先天性纤维肉瘤。一年半后,因局部肿瘤复发,进行了股骨髁上截肢术。