伴有蚓部脑膨出的顶盖小脑发育不全
Tectocerebellar dysraphism with vermian encephalocele.
作者信息
Anik Ihsan, Koc Kenan, Anik Yonca, Yildiz Demir Kursat, Ceylan Savas
机构信息
Department of Neurosurgery, Kocaeli University School of Medicine, Kocaeli, Turkey.
出版信息
J Child Neurol. 2010 Nov;25(11):1411-4. doi: 10.1177/0883073810367828. Epub 2010 May 5.
PMID:20445194
Abstract
Tectocerebellar dysraphism is a very rare malformation associated with encephalocele and tectal deformity. This article presents tectocerebellar dysraphism with a solely vermian content of encephalocele and tectal beaking defined by magnetic resonance imaging (MRI) in a 5-month-old girl who was successfully treated surgically and demonstrated excellent prognosis at the 4-year follow-up.
摘要
顶盖小脑发育不全是一种与脑膨出和顶盖畸形相关的非常罕见的畸形。本文介绍了一名5个月大女童的顶盖小脑发育不全病例，其脑膨出仅包含蚓部组织，且通过磁共振成像（MRI）显示有顶盖鸟嘴样畸形，该女童接受了成功的手术治疗，在4年随访中显示出良好的预后。
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