Inserm U614, Institute for Biomedical Research, Faculty of Medicine, University of Rouen, Rouen, France.
Brain Res. 2010 Jul 23;1345:182-9. doi: 10.1016/j.brainres.2010.05.007. Epub 2010 May 10.
Tauopathies, including Alzheimer's disease (AD), fronto-temporal dementia with parkinsonism linked to chromosome 17 (FTDP-17), Pick's disease and progressive supranuclear palsy, are neurodegenerative disorders neuropathologically characterized by the presence of intraneuronal fibrillary inclusions composed of abnormally phosphorylated-Tau. Tau protein is a neuronal microtubule-associated protein (MAP) involved in microtubules polymerization and stabilization. So far, the molecular mechanisms underlying Tau-mediated cellular toxicity remain elusive. To address the determinants of Tau neurotoxicity, we previously performed a misexpression screening in a Drosophila tauopathy model to identify genetic modifiers of the human Tau-induced neurodegeneration. We identified several components of the actin network as modifiers of Tau V337M-induced neurodegeneration, i.e. Filamin-A, Myosin VI, Paxillin and Transgelin-3. The aim of this study was to assess whether these genetic interactions were associated with a colocalization of the proteins (i) in the brains of patients with Tau pathologies, and (ii) in the brain of transgenic mice overexpressing human mutant Tau. We found that Filamin-A and Myosin VI indeed colocalize with fibrillary Tau protein in AD and FTDP-17 and in Thy-Tau22 transgenic mice.
tau 病,包括阿尔茨海默病 (AD)、与 17 号染色体相关的额颞叶痴呆伴帕金森病 (FTDP-17)、匹克氏病和进行性核上性麻痹,是神经退行性疾病,其神经病理学特征是存在由异常磷酸化 tau 组成的神经元纤维内包涵体。tau 蛋白是一种神经元微管相关蛋白 (MAP),参与微管聚合和稳定。到目前为止,tau 介导的细胞毒性的分子机制仍不清楚。为了研究 tau 介导的细胞毒性的决定因素,我们之前在果蝇 tau 病模型中进行了过表达筛选,以鉴定人类 tau 诱导的神经退行性变的遗传修饰因子。我们鉴定了肌动蛋白网络的几个成分作为 Tau V337M 诱导的神经退行性变的修饰因子,即细丝蛋白 A、肌球蛋白 VI、桩蛋白和 Transgelin-3。本研究旨在评估这些遗传相互作用是否与蛋白 (i) 在 tau 病患者的大脑中,和 (ii) 在过表达人突变 tau 的转基因小鼠的大脑中的共定位有关。我们发现,在 AD 和 FTDP-17 中以及 Thy-Tau22 转基因小鼠中,细丝蛋白 A 和肌球蛋白 VI 确实与纤维状 tau 蛋白共定位。