Trattner A, David M, Rothem A, Ben-David E, Sandbank M
Department of Dermatology, Beilinson Medical Center, Petah Tiqva, Israel.
J Am Acad Dermatol. 1991 May;24(5 Pt 2):822-4. doi: 10.1016/0190-9622(91)70123-j.
Buschke-Ollendorff syndrome is an association of connective tissue nevi and osteopoikilosis that usually appears in the first decades of life. The nevi occur on the trunk and extremities. In a 48-year-old man with this rare syndrome the connective tissue nevus was located on the scalp and was pruritic. Histologically, involvement of the epidermis with cystic dilatation of the hair follicles and an abnormality of mucopolysaccharides were present. The nevi in this syndrome may involve an alteration in the three components of connective tissue to a variable degree.
布施克-奥伦多夫综合征是一种结缔组织痣与播散性豆状皮肤骨瘤的联合病症，通常在生命的头几十年出现。痣发生于躯干和四肢。在一名患有这种罕见综合征的48岁男性中，结缔组织痣位于头皮且伴有瘙痒。组织学上，可见表皮受累伴毛囊囊性扩张以及黏多糖异常。该综合征中的痣可能在不同程度上涉及结缔组织的三种成分的改变。
