Cheng Chun-Chien, Ko Jih-Yang
Department of Orthopedic Surgery, Antai Medical Care Cooperation, Antai Tian-Sheng Memorial Hospital.
Chang Gung Med J. 2010 May-Jun;33(3):266-73.
Congenital dislocation of the knee (CDK) is a very rare condition that comprises a spectrum of deformities from subluxation to complete dislocation. The incidence of CDK is estimated at 1 per 100,000 live births, which is 1% of the incidence of developmental dysplasia of the hip (DDH). Moreover, 40-100% of patients with CDK have additional musculoskeletal anomalies, the most common being DDH and clubfoot. In general, the diagnosis is established immediately after birth according to the position of the knee recurvatum. Treatment with conservative methods at an early stage is most likely to yield successful results. We report here successful treatment of a series of CDK patients with early reduction.
From July 1990 to June 2007, 19 patients with CDK (affecting 25 knees) were treated with early reduction. Of these, 6 knees had dislocation, and 19 had subluxation. Since 1990, treatment has been guided by a protocol that considers patient age and the severity of the condition. In patients examined within 24 hours of birth, early, direct reduction under gentle, persistent manual traction was attempted. Birth history and perinatal course were obtained from medical records. Associated musculoskeletal anomalies were observed and treated after reduction of the knee joint. A Pavlik harness was used for at least 4 months in the concomitant treatment of DDH and CDK. Knee function was graded as excellent, good, fair, or poor. Radiographs were used to assess DDH during follow-up.
After an average follow-up duration of 4.3 years, 18 patients showed an excellent or good outcome. One patient, whose knee could not be reduced, had severe multiple anomalies and died 16 days after birth. Fifteen of the nineteen patients had associated musculoskeletal anomalies, including DDH and foot deformity. Two cases of residual hip dysplasia after Pavlik harnessapplication required an acetabular osteotomy.
For CDK patients, early and direct closed reduction within 24 hours of birth affords outcomes graded as either excellent or good.
先天性膝关节脱位(CDK)是一种非常罕见的疾病,包括从半脱位到完全脱位的一系列畸形。CDK的发病率估计为每10万活产中有1例,占发育性髋关节发育不良(DDH)发病率的1%。此外,40%-100%的CDK患者伴有其他肌肉骨骼异常,最常见的是DDH和马蹄内翻足。一般来说,根据膝关节反屈的位置在出生后立即确诊。早期采用保守方法治疗最有可能取得成功结果。我们在此报告一系列早期复位治疗CDK患者的成功案例。
1990年7月至2007年6月,19例CDK患者(累及25个膝关节)接受了早期复位治疗。其中,6个膝关节为脱位,19个为半脱位。自1990年以来,治疗遵循一个考虑患者年龄和病情严重程度的方案。对于出生后24小时内接受检查的患者,尝试在轻柔、持续的手法牵引下进行早期直接复位。从病历中获取出生史和围产期过程。观察并在膝关节复位后治疗相关的肌肉骨骼异常。在DDH和CDK的联合治疗中,使用 Pavlik 吊带至少4个月。膝关节功能分为优、良、中、差。随访期间使用X线片评估DDH。
平均随访4.3年后,18例患者预后为优或良。1例膝关节无法复位的患者有严重多重异常,出生后16天死亡。19例患者中有15例伴有肌肉骨骼异常,包括DDH和足部畸形。2例使用Pavlik吊带后残留髋关节发育不良的病例需要进行髋臼截骨术。
对于CDK患者,出生后24小时内进行早期直接闭合复位可获得优或良的预后。