André Sónia Traqueia, Valente Carla, Paiva Benedita, Pêgo Alice, Carvalho Lina, Luís A Segorbe
Faculdade de Medicina, Universidade de Coimbra, Departamento de Ciências Pneumológicas e Alergológicas dos Hospitais da Universidade de Coimbra, Coimbra.
Rev Port Pneumol. 2010 May-Jun;16(3):477-82. doi: 10.1016/s0873-2159(15)30044-1.
Epithelioid Hemangioendothelioma (EHE) is a vascular tumour with rare pleural presentation. As there are a small number of cases described in the literature the authors present the case of a 65 -year -old woman, who was admitted to the Emergency Department for a right -sided chest pain, which progressed over 7 months, after a thoracic trauma. The chest X -ray showed signs of a moderate right -sided pleural effusion. A pleural -pulmonary biopsy carried out by toracotomy established the histological diagnosis of EHE of the pleura. Due to the locally advanced stage of the tumour, chemotherapy with carboplatin and etoposide was prescribed and the patient died 6 months later. This case confirms that pleural EHE has an aggressive behaviour, similar to an angiossarcoma, with a median survival of only a few months after diagnosis.
上皮样血管内皮瘤(EHE)是一种血管肿瘤,很少表现为累及胸膜。由于文献中描述的病例数量较少,作者报告了一名65岁女性的病例,该患者因右侧胸痛在胸外伤后7个月进展,被收入急诊科。胸部X线显示中度右侧胸腔积液的迹象。通过开胸手术进行的胸膜-肺活检确立了胸膜EHE的组织学诊断。由于肿瘤处于局部晚期,给予卡铂和依托泊苷化疗,患者6个月后死亡。该病例证实胸膜EHE具有侵袭性,类似于血管肉瘤,诊断后的中位生存期仅为几个月。