Levard G, Boureau M
Clinique chirurgicale, Hôpital Jean-Bernard, CHRU La Milétrie, Poitiers.
Chir Pediatr. 1990;31(6):289-94.
We report seven cases of congenital colonic atresia over a 13 year period (1975-1988). The atresia was located in the ascending or transverse colon (4 cases), or in the descending or sigmoid colon (3 cases). According to Bland-Sutton classification, one patient was a type I, five were either a type II or III, and for the last patient the type was not precise. Three infants had associated malformations: jejunal atresia (case n. 6), intestinal malrotation (case n. 5), and gastroschisis and jejunal atresia. This last patient, in whom jejunal and colonic atresias were autopsy findings, died after a Schuster procedure for gastroschisis closure. The six other neonates survived. Five of them underwent emergency colostomy and delayed anastomosis when general conditions were stable (2 to 10 months after colostomy). The sixth neonate (case n. 2) was treated by colonic resection and primary ileocolic anastomosis. Two patients had postoperative complications, ie, anastomotic leak (case n. 4) or disfunction (case n. 2), which were successfully treated by another operation. The outcome, one year after the onset of the disease, was good for 5 out of the 6 survivors. All these five patients were normally passing stools, once or twice a day, with no abdominal distension. One patient (case n. 6) had a short bowel syndrome secondary to a jejunal atresia, with intermittent watery stools and abdominal distention. We reviewed the 161 cases of colonic atresia from English and French experience since 1960. The overall mortality rate is 25%. Associated malformations and infection are the main causes of death. The rate of anastomotic complications is high (15%).(ABSTRACT TRUNCATED AT 250 WORDS)
我们报告了13年间(1975 - 1988年)7例先天性结肠闭锁病例。闭锁位于升结肠或横结肠(4例),或降结肠或乙状结肠(3例)。根据布兰德 - 萨顿分类,1例患者为I型,5例为II型或III型,最后1例患者的类型不明确。3例婴儿伴有其他畸形:空肠闭锁(病例6)、肠旋转不良(病例5)、腹裂和空肠闭锁。最后这名患者,尸检发现有空肠和结肠闭锁,在施图斯特腹裂修补术后死亡。其他6例新生儿存活。其中5例在一般情况稳定时(结肠造口术后2至10个月)接受了急诊结肠造口术和延期吻合术。第6例新生儿(病例2)接受了结肠切除术和一期回结肠吻合术。2例患者有术后并发症,即吻合口漏(病例4)或功能障碍(病例2),通过再次手术成功治疗。发病一年后的结果,6名幸存者中有5名情况良好。这5名患者每天排便1至2次,大便正常,无腹胀。1例患者(病例6)因空肠闭锁继发短肠综合征,有间歇性水样便和腹胀。我们回顾了自1960年以来英文和法文报道的161例结肠闭锁病例。总体死亡率为25%。合并畸形和感染是主要死亡原因。吻合口并发症发生率很高(15%)。(摘要截选至250字)