Department of Internal Medicine, Louisiana State University Health Sciences Center, Shreveport, LA, USA.
J Clin Hypertens (Greenwich). 2010 Nov;12(11):856-60. doi: 10.1111/j.1751-7176.2010.00359.x. Epub 2010 Aug 20.
Liddle syndrome (LS) is an autosomal dominant disorder due to a gain-of-function mutation in the epithelial Na(+) channel and is perceived to be a rare condition. A cross-sectional study of 149 hypertensive patients with hypokalemia (<4 mmol/dL) or elevated serum bicarbonate (>25 mmol/dL) was conducted at a Veterans' Administration Medical Center Hypertension Clinic in Shreveport, LA. Data on demographics, blood pressure, and select blood tests were collected and expressed as percentages for categoric variables and as mean ± standard deviation (SD) for continuous variables. Patients were diagnosed with likely LS when the plasma renin activity (PRA) was <0.35 μU/mL/h and the aldosterone was <15 ng/dL and likely primary hyperaldosteronism (PHA) with PRA <0.35 μU/mL/h and aldosterone level >15 ng/dL. The cohort included predominantly elderly (67.1±13.4 years), male (96%), and Caucasian (57%) patients. The average blood pressure was 143.8/79.8 mm Hg±27.11/15.20 with 3.03±1.63 antihypertensive drugs. Based on the above criteria, 9 patients (6%) satisfied the criteria for likely LS and 10 patients (6.7%) were diagnosed with likely PHA. In this hypothesis-generating study, the authors detected an unusually high prevalence of biochemical abnormalities compatible with likely LS syndrome from Northwestern Louisiana, approaching that of likely PHA.
利德尔综合征(LS)是一种常染色体显性遗传病,由于上皮钠通道的功能获得性突变所致,被认为是一种罕见疾病。在路易斯安那州什里夫波特的一家退伍军人管理局医疗中心的高血压诊所,对 149 例低钾血症(<4mmol/dL)或高血清碳酸氢盐(>25mmol/dL)的高血压患者进行了横断面研究。收集了人口统计学、血压和一些选择性血液检查的数据,并以百分比表示分类变量,以平均值±标准差(SD)表示连续变量。当血浆肾素活性(PRA)<0.35μU/mL/h且醛固酮<15ng/dL 时,患者被诊断为可能的 LS;当 PRA<0.35μU/mL/h 且醛固酮水平>15ng/dL 时,患者被诊断为可能的原发性醛固酮增多症(PHA)。该队列主要包括老年(67.1±13.4 岁)、男性(96%)和白种人(57%)患者。平均血压为 143.8/79.8mmHg±27.11/15.20mmHg,使用 3.03±1.63 种降压药。根据上述标准,9 例(6%)患者符合可能 LS 的标准,10 例(6.7%)患者被诊断为可能的 PHA。在这项假设生成研究中,作者从路易斯安那州西北部检测到一种异常高的生化异常患病率,与可能的 PHA 相近。