Ceçen Emre, Kaçar-Döger Firuzan, Etensel Barlas
Department of Pediatrics, Adnan Menderes University Faculty of Medicine, Aydin, Turkey.
Turk J Pediatr. 2010 Sep-Oct;52(5):534-7.
Kimura's disease, characterized by a triad of painless subcutaneous masses in the head and neck, prominent eosinophilia and markedly elevated immunoglobulin E levels, is an uncommon idiopathic, chronic inflammatory disease that usually affects young and middle-aged Asian males. Kimura's disease is known usually as a localized process and is an extremely rare cause of generalized lymphadenopathy in children. We report an eight-year-old Turkish boy with Kimura's disease who presented with generalized lymphadenopathy masquerading as malignant lymphoma.
木村病的特征为头颈部出现三联征无痛性皮下肿块、显著嗜酸性粒细胞增多及免疫球蛋白E水平明显升高，是一种罕见的特发性慢性炎症性疾病，通常影响年轻及中年亚洲男性。木村病通常被认为是局限性疾病，是儿童全身性淋巴结病极为罕见的病因。我们报告一例患有木村病的8岁土耳其男孩，其表现为伪装成恶性淋巴瘤的全身性淋巴结病。
