Department of Neurosurgery, Sri Sathya Sai Institute of Higher Medical Sciences, EPIP Area, Whitefield, Bangalore 560066, India.
J Clin Neurosci. 2011 Jul;18(7):986-8. doi: 10.1016/j.jocn.2010.11.025. Epub 2011 May 11.
Primary intracerebral paraganglioma is an unusual entity in the diagnostic armamentarium of the neurosurgeon. Only two patients have been described with a supratentorial intra-parenchymal subtype. We report a 40-year-old man who presented with features of raised intracranial pressure and secondary visual deterioration of short duration. His MRI showed a 2 cm by 2 cm by 2.5 cm, brilliantly enhancing lesion in the left frontal region with flow voids and disproportionate perilesional edema. Magnetic resonance angiography demonstrated a "sun-burst" appearance. The lesion was totally excised, with subsequent resolution of symptoms. Histopathology was reported as a paraganglioma. The systemic workup confirmed the primary intracerebral nature of the lesion. To our knowledge, this report documents a hitherto undescribed, exclusive intraparenchymal location of a rare benign lesion.
原发性颅内副神经节瘤在神经外科的诊断工具中较为少见。仅有两例患者被描述为幕上脑实质内亚型。我们报告了一名 40 岁男性,他表现为颅内压升高和继发性视觉短暂恶化的特征。他的 MRI 显示左额叶有一个 2 厘米×2 厘米×2.5 厘米的病变,呈明亮强化,有流空现象和不成比例的周边水肿。磁共振血管造影显示为“太阳辐射状”外观。病变被完全切除,随后症状缓解。组织病理学报告为副神经节瘤。系统检查证实病变为原发性颅内。据我们所知,本报告记录了一种罕见良性病变的前所未有的、独特的脑实质内位置。