López-Velarde B Pedro, Avila-Vanzzini Nydia, López-Velarde Peña Tatiana, Dabaghi-Richerand Alejandro, López-Soriano Fernando, Espinola-Zavaleta Nilda
Cardiovascular Hemodynamic Department, American British Cowdray Medical Center, Mexico City.
Arch Cardiol Mex. 2011 Jan-Mar;81(1):18-21.
Aneurysms of the sinus of Valsalva (SV) and the atrial septum are a rare association. We report the case of a 28-year-old woman, who was admitted to our department complaining of progressive dyspnea of 10 days of evolution, five hours previous to her admission to the hospital; she presented sudden oppressive anterior chest pain, accompanied by palpitations. The presence of rupture of the right SV to the right atrium was clinically confirmed, by echocardiography and hemodynamic studies. In addition, an associated atrial septal aneurysm was found. She underwent surgical correction through sinusplasty without requiring aortic valve replacement. The patient presented persistent postoperative atrioventricular block, which required a permanent pacemaker. Clinical evolution was satisfactory. To our knowledge, this case is a rare combination of two isolated malformations, without previous events that could explain the rupture of the right SV.
主动脉窦瘤（SV）与房间隔瘤同时存在的情况较为罕见。我们报告了一例28岁女性病例，该患者因进行性呼吸困难10天入院，入院前5小时突发前胸部压榨性疼痛并伴有心悸。经超声心动图和血流动力学检查，临床确诊为右主动脉窦破裂至右心房。此外，还发现了一个合并的房间隔瘤。患者接受了窦瘤修补术，无需置换主动脉瓣。术后患者出现持续性房室传导阻滞，需要植入永久性起搏器。临床恢复情况良好。据我们所知，该病例是两种孤立畸形的罕见组合，此前并无任何事件可解释右主动脉窦破裂的原因。
