Service de Néphrologie et Transplantation, Hôpital Saint-Louis, Université PARIS VII, Paris, France.
Nephrol Dial Transplant. 2012 Jan;27(1):448-9. doi: 10.1093/ndt/gfr433. Epub 2011 Aug 2.
We report here a case with secondary polycythaemia, monoclonal gammopathy of undetermined significance and renal lymphangiectasis revealed by renal failure. Renal failure was probably linked to renal compression by fluid collections. Renal lymphangiectasis is a rare but has already been described in the literature. In addition, its association with a monoclonal paraprotein and polycythaemia seems to be a new clinical entity recently reported in only one patient.
我们在此报告一例由肾衰竭引起的继发性红细胞增多症、意义未明的单克隆丙种球蛋白血症和肾淋巴管扩张症。肾衰竭可能与液体积聚引起的肾脏压迫有关。肾淋巴管扩张症虽然罕见,但已有文献报道。此外,它与单克隆副蛋白和红细胞增多症的关联似乎是一种新的临床实体,最近仅在一名患者中报道。