Department of Children Nephrology, Sophia Children’s Hospital, Erasmus MC, Rotterdam, Netherlands.
Nephrol Dial Transplant. 2011 Nov;26(11):3822-4. doi: 10.1093/ndt/gfr435. Epub 2011 Aug 5.
Encapsulating peritoneal sclerosis (EPS) is a very rare condition in children. Nevertheless, EPS should be considered when a child with a history of peritoneal dialysis (PD) presents with signs of bowel obstruction. We describe a child with post-transplantation EPS and discuss risk factors, diagnosis and treatment options. CT scan should be performed promptly to confirm the diagnosis. Treatment consists of cessation of the PD, if applicable, and adequate nutrition, either parenteral or enteral. Further medical therapy remains controversial but may involve steroids and/or interruption of calcineurin inhibitors.
包裹性腹膜硬化症(EPS)在儿童中非常罕见。然而,当有腹膜透析(PD)病史的儿童出现肠梗阻迹象时,应考虑 EPS。我们描述了一例移植后 EPS 患儿,并讨论了其危险因素、诊断和治疗选择。应及时行 CT 扫描以明确诊断。治疗包括如果适用则停止 PD,并给予充分的营养,肠外或肠内营养。进一步的医学治疗仍存在争议,但可能包括类固醇和/或钙调磷酸酶抑制剂的中断。