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一名法洛四联症修复术后成人的主动脉根部及升主动脉瘤

Aortic root and ascending aortic aneurysm in an adult with a repaired tetralogy of fallot.

作者信息

Kim Tae Sik, Na Chan-Young, Baek Jong Hyun, Yang Jin Sung

机构信息

Department of Thoracic and Cardiovascular Surgery, Sejong General Hospital, Korea.

出版信息

Korean J Thorac Cardiovasc Surg. 2011 Aug;44(4):292-3. doi: 10.5090/kjtcs.2011.44.4.292. Epub 2011 Aug 18.

DOI:10.5090/kjtcs.2011.44.4.292
PMID:22263172
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC3249323/
Abstract

Surgical repair of the tetralogy of Fallot is one of the most successful operations in the treatment of congenital heart diseases. We report the case of a 65-year-old man who had an aortic valve replacement at the time of complete repair of the tetralogy of Fallot at the age of forty-three. He subsequently had progressive aortic root and ascending aorta dilation to 9 cm. The aortic root and ascending aorta replacement was done using a composite valve-graft and was performed along with other procedures. Thus, meticulous follow-up of aortic root and ascending aorta after corrective surgery for tetralogy of Fallot is recommended following initial curative surgery.

摘要

法洛四联症的外科修复是治疗先天性心脏病最成功的手术之一。我们报告一例65岁男性病例,该患者43岁时在法洛四联症完全修复的同时进行了主动脉瓣置换。随后,他的主动脉根部和升主动脉逐渐扩张至9厘米。采用复合瓣膜移植物进行了主动脉根部和升主动脉置换,并同时进行了其他手术。因此,建议在法洛四联症初次根治性手术后,对主动脉根部和升主动脉进行细致的随访。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/fab3/3249323/ab934bb30376/kjtcs-44-292-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/fab3/3249323/53134f66070a/kjtcs-44-292-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/fab3/3249323/ab934bb30376/kjtcs-44-292-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/fab3/3249323/53134f66070a/kjtcs-44-292-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/fab3/3249323/ab934bb30376/kjtcs-44-292-g002.jpg

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本文引用的文献

1
Intrinsic histological abnormalities of aortic root and ascending aorta in tetralogy of Fallot: evidence of causative mechanism for aortic dilatation and aortopathy.法洛四联症患者主动脉根部和升主动脉的内在组织学异常:主动脉扩张和主动脉病变致病机制的证据
Circulation. 2005 Aug 16;112(7):961-8. doi: 10.1161/CIRCULATIONAHA.105.537928. Epub 2005 Aug 8.
2
Aortic dissection late after repair of tetralogy of Fallot.法洛四联症修复术后晚期主动脉夹层。
Int J Cardiol. 2005 Jun 8;101(3):515-6. doi: 10.1016/j.ijcard.2004.03.026.
3
Massive aortic aneurysm and dissection in repaired tetralogy of Fallot; diagnosis by cardiovascular magnetic resonance imaging.
法洛四联症修复术后的巨大主动脉瘤和夹层;心血管磁共振成像诊断
Int J Cardiol. 2005 May 11;101(1):169-70. doi: 10.1016/j.ijcard.2004.05.037.
4
Progressive aortic root dilatation in adults late after repair of tetralogy of Fallot.法洛四联症修复术后晚期成人患者的主动脉根部进行性扩张。
Circulation. 2002 Sep 10;106(11):1374-8. doi: 10.1161/01.cir.0000028462.88597.ad.
5
Aortic valve replacement after repair of pulmonary atresia and ventricular septal defect or tetralogy of Fallot.肺动脉闭锁合并室间隔缺损或法洛四联症修复术后的主动脉瓣置换术。
J Thorac Cardiovasc Surg. 1997 Apr;113(4):736-41. doi: 10.1016/S0022-5223(97)70232-0.