一名患有卡塔格内综合征的女孩在Fontan手术后5年发生了塑料支气管炎。

Plastic bronchitis developing 5 years after Fontan procedure in a girl with Kartagener's syndrome.

作者信息

Nawa Tomohiro, Yokozawa Masato, Takamuro Motoki, Kasuga Ai

机构信息

Department of Pediatric Cardiology, Hokkaido Medical Center for Child Health and Rehabilitation, Sapporo, Japan.

出版信息

Pediatr Cardiol. 2012 Jun;33(5):846-9. doi: 10.1007/s00246-012-0235-6. Epub 2012 Feb 14.

DOI:10.1007/s00246-012-0235-6

PMID:22331057

Abstract

Although rare, plastic bronchitis (PB) is an important early complication after Fontan procedure. Kartagener's syndrome is characterized by mucociliary dysfunction of the respiratory tract and has a triad of features, including situs inversus totalis, chronic sinusitis, and bronchiectasia. We experienced PB in a patient with Kartagener's syndrome 5 years after Fontan procedure.

摘要

虽然罕见，但塑料支气管炎（PB）是Fontan手术后重要的早期并发症。卡塔格内综合征的特征是呼吸道的黏液纤毛功能障碍，具有三联征，包括完全性内脏转位、慢性鼻窦炎和支气管扩张。我们遇到1例Fontan手术后5年出现塑料支气管炎的卡塔格内综合征患者。