Kittur M A, Padgett J, Drake D
Dept. of Oral and Maxillofacial Surgery, Morriston Hospital, Swansea, UK.
Br J Oral Maxillofac Surg. 2013 Jan;51(1):e6-8. doi: 10.1016/j.bjoms.2012.01.015. Epub 2012 Feb 15.
Beckwith-Wiedemann syndrome (BWS) is a rare congenital disease of low prevalence. Its most common feature is macroglossia, being present in most cases. Clinically macroglossia can compromise the airway, cause dysphagia, drooling and poor cosmesis. Functionally it can cause dentoskeletal discrepancy, protrusion of teeth, and speech abnormalities leading significant psychological issues both with the patient and their families. Surgical excision remains the mainstay of management and a variety of techniques have been described. Because of the high vascularity of the tongue, intra-operative blood loss could be significant and have high morbidity in the pediatric patient. We present a technique for tongue reduction in macroglossia associated with BWS using the Ultrasonic Dissector (Harmonic Scalpel). The principles of Ultrasonic dissection are discussed along with the potential advantages of the technique.
贝克威思-维德曼综合征（BWS）是一种罕见的先天性疾病，发病率较低。其最常见的特征是巨舌症，多数病例中都存在。临床上，巨舌症会影响气道，导致吞咽困难、流口水和美观不佳。在功能方面，它会导致牙颌面不协调、牙齿前突和言语异常，给患者及其家庭带来严重的心理问题。手术切除仍然是主要的治疗方法，并且已经描述了多种技术。由于舌头血管丰富，术中失血可能较多，并且在儿科患者中发病率较高。我们介绍一种使用超声刀治疗与BWS相关的巨舌症的缩舌技术。同时讨论了超声刀切割的原理以及该技术的潜在优势。
