Department of Dermatology, Fukushima Medical University, Fukushima, Japan.
Australas J Dermatol. 2012 May;53(2):e32-3. doi: 10.1111/j.1440-0960.2010.00719.x. Epub 2010 Nov 29.
We report a case of systemic sclerosis with interstitial pneumonia and severe pulmonary hypertension treated with bosentan, an endothelin receptor antagonist. Within a short period of administration of the bosentan the skin sclerosis improved.
我们报告了 1 例系统性硬化症伴间质性肺炎和严重肺动脉高压患者,使用内皮素受体拮抗剂波生坦进行治疗。在给予波生坦治疗的短时间内,皮肤硬化得到改善。