Jain Upendra, Thakur Gagan, Kallury Amitabh
Department of Orthodontia, People's College of Dental Sciences and Research Centre, Bhopal, Madhya Pradesh, India.
BMJ Case Rep. 2011 Oct 11;2011:bcr0820114665. doi: 10.1136/bcr.08.2011.4665.
Binder syndrome or maxillonasal dysplasia is an uncommon developmental anomaly affecting primarily the anterior part of the maxilla and nasal complex. The characteristic findings are a failure of development in the premaxillary area with associated deformities of the nasal skeleton and the overlying soft tissues. Affected individuals typically have an unusually flat, underdeveloped midface (midfacial hypoplasia), with an abnormally short nose and flat nasal bridge, underdeveloped upper jaw, relatively protruding lower jaw and/or a 'reverse overbite' (or class III malocclusion). A 16-year-old female reported to clinic with chief complaint of facial deformity, on examination patient had classical feature of maxillonasal dysplasia. A brief review of the condition and the proposed multi-disciplinary treatment plan is discussed.
宾德综合征或上颌鼻发育不全是一种罕见的发育异常,主要影响上颌和鼻复合体的前部。其特征性表现是前颌骨区域发育不良,并伴有鼻骨和覆盖其上的软组织畸形。受影响的个体通常有异常扁平、发育不全的中面部(面中部发育不全),鼻子异常短且鼻梁扁平,上颌发育不全,下颌相对突出和/或“反覆咬合”(或III类错牙合)。一名16岁女性因面部畸形为主诉前来就诊,检查发现患者具有上颌鼻发育不全的典型特征。本文讨论了对该病症的简要回顾以及拟议的多学科治疗方案。