Granata C, Magni E, Merlini L, Cervellati S
Servizio di Recupero e Rieducazione Funzionale, Istituto Ortopedico Rizzoli, Bologna.
Chir Organi Mov. 1990 Apr-Jun;75(2):177-84.
Hip conditions in 49 patients affected with spinal muscular atrophy were studied: 35 of these were affected with the intermediate form of the disease (patients were able to sit but not walk), and 14 with the mild form (patients were able to walk). The Perkins method was used to measure the migration percentage of the femoral head. Thirty-one percent of the patients affected by the intermediate form of the disease had normal hips, 38% had unilateral or bilateral subluxation, 11% had hip dislocation. In the mild form of the disease, 50% of the patients had normal hips, 28% had unilateral or bilateral subluxation, and 22% had a hip dislocation. In the intermediate form of the disease there was a linear correlation between migration percentage and age, and between migration percentage and scoliosis. In the patients affected with the mild form of the disease who were able to walk, and in the patients affected with the intermediate form and fitted with orthoses who were able to stand, or to walk, there was no hip dislocation. Hence, walking with or without orthoses seems to be an important factor in preventing hip dislocation.
对49例脊髓性肌萎缩症患者的髋关节状况进行了研究：其中35例为疾病的中间型（患者能够坐但不能行走），14例为轻型（患者能够行走）。采用珀金斯方法测量股骨头的移位百分比。疾病中间型患者中，31%髋关节正常，38%有单侧或双侧半脱位，11%有髋关节脱位。在疾病轻型患者中，50%髋关节正常，28%有单侧或双侧半脱位，22%有髋关节脱位。在疾病中间型中，移位百分比与年龄以及移位百分比与脊柱侧弯之间存在线性相关性。在能够行走的轻型疾病患者以及佩戴矫形器能够站立或行走的中间型疾病患者中，没有髋关节脱位情况。因此，无论是否佩戴矫形器行走似乎都是预防髋关节脱位的一个重要因素。
