Vachhani Jay A, Fassett Daniel R
Department of Neurosurgery, Illinois Neurological Institute, University of Illinois College of Medicine, Peoria, Illinois.
Surg Neurol Int. 2012;3:80. doi: 10.4103/2152-7806.98525. Epub 2012 Jul 14.
Neurenteric cysts are benign tumors of the central nervous system (CNS) that represent 0.3% to 0.5% of all spinal cord tumors. They are usually extramedullary and found in the lower cervical and thoracic spine. Only 12.2% of neurenteric cysts are documented to be intramedullary.
The authors report a case of a 35-year-old female that presented with progressive weakness and loss of coordination in her legs. Magnetic resonance imaging (MRI) showed an intramedullary cystic lesion in the thoracolumbar region and a low-lying conus medullaris suggesting tethered cord. The patient was taken to the operating room for detethering of her spinal cord and resection of the lesion. Pathologic examination of the tissue confirmed the diagnosis of a neurenteric cyst.
A search of the literature since the advent of MRI showed 29 published cases of intramedullary neurentic cysts. Of the 24 published cases with a follow-up MRI, the average recurrence rate was 25% with a mean follow up of 51 months.
神经肠囊肿是中枢神经系统（CNS）的良性肿瘤，占所有脊髓肿瘤的0.3%至0.5%。它们通常位于髓外，多见于下颈椎和胸椎。仅有12.2%的神经肠囊肿被记录为髓内囊肿。
作者报告一例35岁女性病例，该患者出现进行性腿部无力和协调性丧失。磁共振成像（MRI）显示胸腰段有一髓内囊性病变，圆锥低位提示脊髓拴系。患者被送往手术室进行脊髓松解和病变切除。组织病理学检查确诊为神经肠囊肿。
自MRI出现以来检索文献发现29例已发表的髓内神经肠囊肿病例。在24例有随访MRI的已发表病例中，平均复发率为25%，平均随访时间为51个月。
