Department of Neurology and Tianjin Neurological Institute, Tianjin Medical University General Hospital, Tianjin, 300052, China.
Neurosci Bull. 2012 Oct;28(5):469-74. doi: 10.1007/s12264-012-1256-0. Epub 2012 Jul 4.
To evaluate the frequency, distribution and clinical significance of the antibodies to the fetal and/or adult acetylcholine receptor (AChR) in patients with myasthenia gravis (MG).
AChR antibodies were detected by cell-based assay in the serum of ocular MG (OMG) (n = 90) and generalized MG (GMG) patients (n = 110). The fetal-type (2α: β: γ: δ) and adult-type (2α: β: ε: δ) AChR were used as antigens, and their relevance to disease presentation was assessed.
The overall frequencies of anti-adult and anti-fetal AChR antibodies were similar in all 200 patients examined, with 14 having serum specific to the AChR-Γ subunit, and 22 to the AChR-ε subunit. The overall sensitivity when using the fetal and adult AChR antibodies was higher than that when using the fetal AChR antibody only (P = 0.015). Compared with OMG patients, the mean age at disease onset and the positive ratio of antibodies to both isoforms of the AChR were significantly higher in patients who subsequently progressed to GMG. Older patients and patients with both anti-fetal and anti-adult AChR antibodies had a greater risk for developing generalized disease [odds ratio (OR), 1.03; 95% confidence interval (CI), 1.01-1.06 and OR, 5.09; 95% CI, 2.23-11.62].
Using both fetal- and adult-type AChRs as the antigens may be more sensitive than using either subtype. Patients with serum specific to both isoforms are at a greater risk of progressing to GMG. Patients with disease onset at an advanced age appear to have a higher frequency of GMG conversion.
评估抗乙酰胆碱受体(AChR)抗体在重症肌无力(MG)患者中的频率、分布和临床意义。
采用细胞基础检测法检测 90 例眼肌型 MG(OMG)和 110 例全身型 MG(GMG)患者血清中的 AChR 抗体。使用胎儿型(2α:β:γ:δ)和成人型(2α:β:ε:δ)AChR 作为抗原,并评估其与疾病表现的相关性。
在所有 200 例患者中,抗成人和抗胎儿 AChR 抗体的总频率相似,14 例患者血清特异性针对 AChR-Γ 亚单位,22 例患者血清特异性针对 AChR-ε 亚单位。使用胎儿和成人 AChR 抗体的总体敏感性高于仅使用胎儿 AChR 抗体(P = 0.015)。与 OMG 患者相比,随后发展为 GMG 的患者的发病年龄和两种 AChR 同工型抗体的阳性率均显著更高。年龄较大的患者和同时具有抗胎儿和抗成人 AChR 抗体的患者发生全身性疾病的风险更高[比值比(OR),1.03;95%置信区间(CI),1.01-1.06 和 OR,5.09;95%CI,2.23-11.62]。
使用胎儿型和成人型 AChR 作为抗原可能比使用任何一种亚型都更敏感。具有两种同工型抗体的血清患者更有可能发展为 GMG。发病年龄较大的患者似乎更频繁地转化为 GMG。