Barranhas Adriana Dias, Dias Márcia Cláudia, Dos Santos Alair Augusto Sarmet Moreira Damas, Marchiori Edson, Nacif Marcelo Souto
Radiology Department, Federal Fluminense University School of Medicine, HUAP 2º andar, Rua Marquês do Paraná s/n,, Centro - Niterói, RJ, Brazil.
J Med Case Rep. 2012 Oct 19;6:357. doi: 10.1186/1752-1947-6-357.
Annular subvalvular pseudoaneurysm is a rare example of left ventricle aneurysm described predominantly in young African people. These aneurysms are divided into two different types, namely, submitral or subaortic, with subaortic being the less frequent kind. The subaortic type is most often localized in the mitral-aortic intervalvular fibrosa. To the best of our knowledge, this is the first report of a mitral-aortic intervalvular fibrosa pseudoaneurysm associated with coarctation of the aorta, anomalous pulmonary venous return, bicuspid aortic valve and patent ductus arteriosus diagnosed by cardiovascular magnetic resonance.
We report the case of a 15-year-old African-American boy with a history of mild chest trauma who underwent echocardiographic evaluation as part of an out-patient work up. The echocardiogram was suspicious for the presence of mitral-aortic intervalvular fibrosa pseudoaneurysm and cardiovascular magnetic resonance was then performed to better characterize this finding. In addition to confirming the presence of the aneurysm, cardiovascular magnetic resonance also revealed coarctation of the aorta, a bicuspid aortic valve, and anomalous pulmonary venous return.
In our case, cardiovascular magnetic resonance was helpful in: (a) making a definite diagnosis of mitral-aortic intervalvular fibrosa pseudoaneurysm and its borders, which was not clear with an echocardiogram examination; and (b) illustrating additional associated congenital anomalies including the anomalous pulmonary venous return.
瓣环下假性动脉瘤是左心室动脉瘤的一种罕见类型,主要见于年轻非洲人群。这些动脉瘤分为两种不同类型,即二尖瓣下型或主动脉瓣下型,其中主动脉瓣下型较为少见。主动脉瓣下型最常位于二尖瓣 - 主动脉瓣间纤维组织。据我们所知,这是首例通过心血管磁共振诊断的与主动脉缩窄、肺静脉异位引流、二叶式主动脉瓣和动脉导管未闭相关的二尖瓣 - 主动脉瓣间纤维组织假性动脉瘤的报告。
我们报告一例15岁非裔美国男孩,有轻度胸部外伤史,作为门诊检查的一部分接受了超声心动图评估。超声心动图怀疑存在二尖瓣 - 主动脉瓣间纤维组织假性动脉瘤,随后进行了心血管磁共振检查以更好地明确这一发现。除了确认动脉瘤的存在外,心血管磁共振还显示了主动脉缩窄、二叶式主动脉瓣和肺静脉异位引流。
在我们的病例中,心血管磁共振有助于:(a)明确诊断二尖瓣 - 主动脉瓣间纤维组织假性动脉瘤及其边界,而超声心动图检查时边界并不清晰;(b)显示其他相关的先天性异常,包括肺静脉异位引流。