[Malignant angioendotheliomatosis].

Malignant angioendotheliomatosis is one of the terms used to describe the appearance of neoplastic cells resembling endothelium within the lumen of small and medium-sized blood vessels, mainly in the cerebral and meningeal vascular beds. A fatal systemic disease with dementia as the leading neurological manifestation may be associated with these pathological findings. Only recently has it become evident that this disease is a unique intravascular form of large cell lymphoma, affecting mainly the cerebral blood vessels but also present in the lumen of many small and medium-sized blood vessels in the systemic circulation.