经心血管磁共振成像诊断为孤立性二尖瓣裂伴严重反流导致左下肺静脉静脉曲张。

Isolated cleft mitral valve with severe regurgitation resulting in a left inferior pulmonary vein varix diagnosed from cardiovascular magnetic resonance imaging.

作者信息

Teo Lynette L S, Hia Cindy P P, Ling L H, Quek S C

机构信息

Department of Diagnostic Imaging, National University Hospital, 5 Lower Kent Ridge Road, Singapore, 119074, Singapore.

出版信息

Pediatr Cardiol. 2013 Apr;34(4):1055-6. doi: 10.1007/s00246-012-0573-4. Epub 2012 Nov 10.

DOI:10.1007/s00246-012-0573-4

PMID:23143311

Abstract

Isolated cleft mitral valve (ICMV) is a rare entity not known to be related to pulmonary atresia with ventricular septal defect (PA-VSD). This report describes the use of cardiovascular magnetic resonance (CMR) imaging to diagnose ICMV in a patient with repaired PA-VSD who presented with incidental severe mitral regurgitation (MR) on follow-up echocardiography. An associated pulmonary varix secondary to the severe MR also was shown by CMR.

摘要

孤立性二尖瓣裂（ICMV）是一种罕见的疾病，目前尚不清楚其与室间隔缺损合并肺动脉闭锁（PA-VSD）有关。本报告描述了一名PA-VSD修补术后患者的情况，该患者在随访超声心动图检查时意外发现重度二尖瓣反流（MR），通过心血管磁共振（CMR）成像诊断为ICMV。CMR还显示了重度MR继发的相关肺静脉曲张。