Clin Neuroradiol. 2013 Sep;23(3):243-7. doi: 10.1007/s00062-012-0183-9. Epub 2012 Dec 4.
Hemangioblastoma (HBL) within the central nervous system is a benign vascular neoplasm that usually occurs in the cerebellum. Supratentorial occurrence of HBL is an extremely rare event. Till date, approximately 129 cases of supratentorial HBL have been reported in the literature. Here, we present three new cases of supratentorial hemangioblatomas, one of which was found to have the lesions in a unique location of the choroidal fissure. The clinical, histopathological, and neuroradiological characteristics, as well as management of this rare disease are discussed with a review of the pertinent literature.
中枢神经系统内的血管母细胞瘤(HBL)是一种良性血管肿瘤,通常发生在小脑。幕上 HBL 的发生是一种极其罕见的事件。迄今为止,文献中约有 129 例幕上 HBL 报道。在这里,我们报告了 3 例新的幕上血管母细胞瘤病例,其中 1 例病变位于脉络膜裂的独特位置。讨论了这种罕见疾病的临床、组织病理学和神经影像学特征以及治疗方法,并复习了相关文献。