Tian Zhuang, Fang Li-Gang, Liu Yong-Tai, Zhang Shu-Yang
Department of Cardiology, Peking Union Medical College Hospital, Chinese Academy of Medical Science & Peking Union Medical College, China.
Intern Med. 2013;52(2):233-6. doi: 10.2169/internalmedicine.52.7643. Epub 2013 Jan 15.
Anomalous origin of the left coronary artery from the pulmonary artery (ALCAPA) is a rare congenital malformation. It is unusual for an ALCAPA patient to survive to adulthood. We present a case of an asymptomatic 54-year-old woman with this syndrome in which visualization of a markedly enlarged and tortuous right coronary artery and intercoronary collaterals by echocardiography raises suspicion for this disease and subsequently guides a step-by-step diagnosis. The patient lives well without surgery 3 years after diagnosis.
左冠状动脉起源于肺动脉(ALCAPA)是一种罕见的先天性畸形。患有ALCAPA的患者存活至成年期并不常见。我们报告一例54岁无症状女性患有此综合征的病例,其中超声心动图显示右冠状动脉明显增粗迂曲以及冠状动脉间侧支循环,这引起了对该疾病的怀疑,并随后指导了逐步诊断。该患者在诊断后3年未经手术,生活良好。