Surendar Marappan Natarajan, Pandey Ramesh Kumar, Khanna Richa
Department of Pedodontics with Preventive Dentistry, King George's Medical University, Lucknow, Uttar Pradesh, India.
BMJ Case Rep. 2013 Jan 22;2013:bcr2012008259. doi: 10.1136/bcr-2012-008259.
Taurodontism is a rare dental anomaly in which there is an enlarged pulp chamber at the expense of roots with apical displacement of the pulpal floor, giving it a rectangular shape. It is caused by the failure of Hertwig's epithelial root sheath to invaginate at the proper horizontal level. Taurodontism has been reported as an intraoral feature of several syndromes like Down syndrome, Klinefelter syndrome, Smith-Magenis syndrome, Hurler syndrome, etc. Association of taurodontism with hypodontia in permanent dentition has also been reported. Taurodontism in primary dentition and its association with hypodontia is very rarely reported in the literature. The present case illustrates bilateral taurodontism of primary mandibular molars with hypodontia in maxilla.
牛牙症是一种罕见的牙齿发育异常，其牙髓腔增大，牙根部分减少，髓室底向根尖移位，使牙髓腔呈长方形。它是由赫特维希上皮根鞘未能在适当的水平向内凹陷引起的。牛牙症已被报道为几种综合征的口腔内特征，如唐氏综合征、克兰费尔特综合征、史密斯-马吉尼斯综合征、黏多糖贮积症Ⅰ型等。恒牙列中牛牙症与牙缺失的关联也有报道。乳牙列中的牛牙症及其与牙缺失的关联在文献中报道极少。本病例展示了双侧下颌乳磨牙牛牙症伴上颌牙缺失。
