Shanker Vinay, Gupta Mudita
Department of Dermatology, Venereology and Leprosy, I.G.M.C, Shimla, India.
Indian Dermatol Online J. 2013 Jan;4(1):40-2. doi: 10.4103/2229-5178.105470.
Dermatopathia pigmentosa reticularis is a rare ectodermal dysplasia with a triad of generalized reticulate hyperpigmentation, noncicatricial alopecia, and onychodystrophy. We report a case of a 21 year old woman who had generalized reticulate pigmentation, diffuse noncicatricial alopecia and onychodystrophy of finger and toe nails. Along with this triad she had palmoplantar keratoderma and poorly developed dermatoglyphics. There was no evidence of involvement of other ectodermally derived organ.
网状色素性皮病是一种罕见的外胚层发育不良疾病,具有全身性网状色素沉着、非瘢痕性脱发和甲营养不良三联征。我们报告一例21岁女性患者,她有全身性网状色素沉着、弥漫性非瘢痕性脱发以及手指和脚趾甲的甲营养不良。除了这三联征外,她还有掌跖角化病和发育不良的皮纹。没有证据表明其他外胚层来源的器官受累。