Department of Medicine, Amyloidosis Center, Boston University School of Medicine and Boston Medical Center, Boston, MA, USA.
Amyloid. 2013 Jun;20(2):127-30. doi: 10.3109/13506129.2013.775644. Epub 2013 Mar 6.
AL amyloidosis presenting as a solitary mediastinal mass is a rare occurrence, with only a few cases reported in the literature. We describe a case of a man presenting with a mediastinal mass diagnosed as amyloidosis, confirmed by mass spectrometry to consist of lambda light chains. Here we review the literature and discuss treatment options for this rare entity.
孤立性纵隔肿块的淀粉样变性较为罕见,文献中仅有少数病例报道。我们描述了一例以纵隔肿块为表现的男性病例,经质谱法证实为淀粉样变性,由 lambda 轻链组成。在此,我们对该罕见实体的文献进行复习并讨论其治疗选择。