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动脉导管未闭合并艾森曼格综合征

Patent ductus arteriosus with Eisenmenger syndrome.

作者信息

Moustafa Sherif, Patton David J, Balon Yvonne, Connelly Michael S, Alvarez Nanette

机构信息

Adult Congenital Heart Disease Clinic, Peter Lougheed Hospital, Division of Cardiovascular Diseases, University of Calgary, Calgary, AB, Canada; Division of Cardiovascular Diseases, Prince Salman Heart Center, King Fahad Medical City, Riyadh, Saudi Arabia.

出版信息

Heart Lung Circ. 2013 Nov;22(11):968-9. doi: 10.1016/j.hlc.2013.03.071. Epub 2013 Apr 11.

Abstract

Herein we report a 21 year-old woman with a previously documented patent ductus arteriosus and Eisenmenger physiology. She presented with increasing cyanosis and exercise intolerance which could be explained by a new finding of right to left shunting through an interatrial communication. She was started on Bosentan therapy aiming to reduce the pulmonary pressure with consideration for heart-lung transplantation should any further deterioration occur.

摘要

在此,我们报告一名21岁女性,既往有动脉导管未闭及艾森曼格综合征生理学改变的记录。她出现了进行性发绀和运动不耐受,这可以通过一项新发现来解释,即存在经心房交通的右向左分流。开始给予波生坦治疗,旨在降低肺动脉压力,并考虑到若病情进一步恶化则进行心肺移植。

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