Wada Keita, Takaori Kyoichi, Traverso L William, Hruban Ralph H, Furukawa Toru, Brentnall Teresa A, Hatori Takashi, Sano Keiji, Takada Tadahiro, Majima Yoshiyuki, Shimosegawa Tooru
Department of Surgery, Teikyo University School of Medicine, 2-11-1 Kaga Itabashi-ku, Tokyo, 173-8605, Japan.
J Hepatobiliary Pancreat Sci. 2013 Aug;20(6):557-66. doi: 10.1007/s00534-013-0611-5.
Pancreatic cancer is still a highly lethal disease with a 5-year survival rate of approximately 5 %. Early detection offers one of the best hopes for improving survival. Previous cohort studies and case-control studies showed that 4-10 % of pancreatic cancers have a hereditary basis, and individuals with a family history have an increased risk of developing pancreatic and extra-pancreatic malignancies. Since individuals with a family history of pancreatic cancer and those with a known genetic syndrome that predisposes to pancreatic cancer will be the first to benefit from early detection tests as they become available, familial pancreatic cancer (FPC) registries have been established in the US and Europe, but not yet in Japan. Such registries form the basis for epidemiological studies, clinical trials, and basic research on familial pancreatic cancer. There is a need for FPC registries in Japan as cancer risk varies among different populations and discoveries made in Western populations may not translate to the Japanese population. These registries in Japan will align with ongoing international efforts and add to a better understanding of the natural history, risk factors, screening strategies, and responsible genes, for improving survival of this dismal disease.
胰腺癌仍然是一种致死率很高的疾病,5年生存率约为5%。早期检测是提高生存率的最大希望之一。以往的队列研究和病例对照研究表明,4%-10%的胰腺癌有遗传基础,有家族病史的个体患胰腺和胰腺外恶性肿瘤的风险增加。由于有胰腺癌家族病史的个体以及患有已知的易患胰腺癌遗传综合征的个体将最先从早期检测试验中受益,美国和欧洲已经建立了家族性胰腺癌(FPC)登记处,但日本尚未建立。此类登记处构成了家族性胰腺癌流行病学研究、临床试验和基础研究的基础。日本需要建立FPC登记处,因为不同人群的癌症风险各不相同,西方人群的研究发现可能不适用于日本人群。日本的这些登记处将与正在进行的国际努力保持一致,并有助于更好地了解这种可怕疾病的自然史、风险因素、筛查策略和相关基因,以提高生存率。