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[骨软骨瘤病性气管支气管病]

[Tracheobronchopathia osteochondroplastica].

作者信息

Potthoff H J, Schubotz R

机构信息

Abteilung Innere Medizin, Kreiskrankenhaus Mayen.

出版信息

Dtsch Med Wochenschr. 1990 Jul 6;115(27):1059-62. doi: 10.1055/s-2008-1065121.

DOI:10.1055/s-2008-1065121
PMID:2364884
Abstract

A 70-year-old woman developed increasing dyspnoea and hoarseness without stridor. Bronchoscopy revealed the characteristic picture of a "rock-garden" with multiple whitish irregularly shaped nodules in the distal two third of the trachea, except the pars membranacea, involving the right-sided bronchial system to the origin of the lower-lobe bronchus, and the left main bronchus. The diagnosis of tracheobronchopathia osteochondroplastica was confirmed histologically: primary tracheobronchial amyloidosis was excluded. Tomography of the tracheobronchial tree demonstrated the findings, but a plain chest X-ray did not. The symptoms in this patient were not, however, caused by tracheobronchopathia osteochondroplastica but by concomitant pulmonary emphysema and acute laryngitis and were improved after symptomatic treatment of the laryngitis.

摘要

一名70岁女性出现进行性呼吸困难和声音嘶哑,但无喘鸣。支气管镜检查显示气管远端三分之二(除膜部外)呈现“石花园”样特征性表现,有多个白色不规则形结节,累及右侧支气管系统直至下叶支气管起始处以及左主支气管。经组织学检查确诊为骨软骨化气管支气管病:排除原发性气管支气管淀粉样变。气管支气管树断层扫描显示了这些表现,但胸部X线平片未显示。然而,该患者的症状并非由骨软骨化气管支气管病引起,而是由合并的肺气肿和急性喉炎所致,在对喉炎进行对症治疗后症状有所改善。

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