Takahashi Kuniyuki, Yamamoto Yutaka, Ohshima Shinsuke, Morita Yuka, Takahashi Sugata
Department of Otolaryngology, Niigata University, Faculty of Medicine, Japan.
Department of Otolaryngology, Niigata University, Faculty of Medicine, Japan.
Auris Nasus Larynx. 2014 Feb;41(1):93-6. doi: 10.1016/j.anl.2013.04.007. Epub 2013 May 18.
To describe primary paraganglioma in the facial nerve canal and discuss the characteristics of facial nerve paraganglioma in contrast with other tumors.
A 23-year-old man developed gradually progressive right facial palsy as the initial symptom. One year later, he exhibited hearing loss without tinnitus in his right ear. CT demonstrated an enlarged facial nerve canal with irregular bony erosion of the circumference. MRI showed a well-enhanced heterogeneous mass with hypo-intensity spots inside it. During surgery, a blood-rich tumor was observed along the facial nerve: however, extensive bleeding interfered with tumor removal. The surgical specimen demonstrated paraganglioma. The tumor was completely removed in the second surgery in combination with arterial embolization. Facial nerve function was reconstructed with a free muscle flap more than one year following resection.
Because paraganglioma is a blood-rich tumor, it is important to perform angiography and embolization. If preoperative facial nerve palsy is demonstrated, careful management of facial nerve function is needed. Paraganglioma must be considered in the differential diagnosis of a facial nerve tumor.
描述面神经管内原发性副神经节瘤,并与其他肿瘤对比讨论面神经副神经节瘤的特征。
一名23岁男性以逐渐进展的右侧面神经麻痹为首发症状。1年后,他出现右耳听力丧失但无耳鸣。CT显示面神经管扩大,周围骨质呈不规则侵蚀。MRI显示一个强化良好的不均匀肿块,内部有低信号灶。手术中,沿面神经观察到一个血供丰富的肿瘤;然而,广泛出血妨碍了肿瘤切除。手术标本显示为副神经节瘤。在第二次手术中结合动脉栓塞将肿瘤完全切除。切除后一年多,用游离肌瓣重建面神经功能。
由于副神经节瘤是血供丰富的肿瘤,进行血管造影和栓塞很重要。如果术前出现面神经麻痹,需要对面神经功能进行仔细管理。在面神经肿瘤的鉴别诊断中必须考虑副神经节瘤。