Division of Plastic Surgery, School of Medicine, University of California-Irvine, CA, USA.
Aesthet Surg J. 2013 Aug 1;33(6):799-808. doi: 10.1177/1090820X13495692. Epub 2013 Jul 9.
Congenital deficiencies of the alar cartilages are rare and often visible at birth but can occasionally present later.
The authors review the anatomical development and discuss the incidence and treatment of congenital defects within the alar cartilages seen in rhinoplasty cases.
The charts of 869 consecutive patients who underwent open rhinoplasty were retrospectively reviewed, and 8 cases of congenital defects of the alar cartilage within the middle crura were identified. Intraoperative photographs were taken of the alar deformities, and each patient underwent surgical correction. To simplify analysis, a classification of the defects was developed. A division was a cleft in the continuity of the alar cartilage with the 2 ends separate. A gap was a true absence of cartilage ranging from 1 to 4 mm, which can be accurately assessed in unilateral cases. A segmental loss was a defect greater than 4 mm.
The 8 cases of deformity could be classified as 4 divisions, 3 gaps, and 1 segmental loss. None of the patients had a history of prior nasal trauma or nasal surgery. Six patients were women and 2 patients were men. In all cases, adequate projection and stability were achieved with a columellar strut. Asymmetry was minimized through concealer or tip grafts. There were no complications.
Surgeons performing rhinoplasty surgery will encounter and should be prepared to deal with unexpected congenital defects of the alar cartilage. These defects within the middle crura will require stabilization with a columellar strut and, often, coverage with a concealer tip graft. We speculate that the cause of these defects is a disruption of the hedgehog signals that may arrest the condensation or block the differentiation of the underlying neural crest cells.
鼻翼软骨先天缺损较为罕见,通常在出生时即可发现,但也可能会在后期出现。
作者回顾了鼻翼软骨的解剖学发育过程,并讨论了在鼻整形手术中遇到的鼻翼软骨先天性缺陷的发生率和治疗方法。
回顾性分析了 869 例连续接受开放式鼻整形术患者的病历,发现了 8 例鼻翼软骨中外侧脚的先天性缺陷。对鼻翼畸形的术中照片进行了拍摄,并对每位患者进行了手术矫正。为了简化分析,作者制定了一种缺陷分类方法。分裂是指鼻翼软骨连续性中断,两端分离;间隙是指软骨确实缺失,范围为 1 至 4 毫米,在单侧情况下可以准确评估;节段性缺失是指缺损大于 4 毫米。
8 例畸形可分为 4 例分裂、3 例间隙和 1 例节段性缺失。患者均无既往鼻部外伤或鼻部手术史。6 例为女性,2 例为男性。所有患者均通过鼻中隔支撑体获得了足够的外展和稳定性。通过隐蔽或鼻尖移植物来最小化不对称。无并发症发生。
行鼻整形手术的外科医生会遇到并应准备好处理鼻翼软骨的意外先天性缺陷。这些中外侧脚的缺陷需要通过鼻中隔支撑体来稳定,并常常需要用隐蔽或鼻尖移植物来覆盖。我们推测这些缺陷的原因是 Hedgehog 信号中断,可能会阻止鼻翼软骨的凝聚或阻止其下方神经嵴细胞的分化。