Hamidian-Jahromi Alireza, Carroll Jonathan D, Doucet Linda D, Zhang Wayne W
Division of Vascular and Endovascular Surgery, Department of Surgery, Louisiana State University Health Sciences Center, Shreveport, LA.
Ann Vasc Surg. 2013 Nov;27(8):1182.e1-4. doi: 10.1016/j.avsg.2013.04.007. Epub 2013 Sep 5.
Turner's syndrome (TS) has been documented as the most common cause of aortic dissection in young women. However, little attention from vascular surgery has been paid to these patients. We report the first case of ruptured type B aortic dissection with aberrant right subclavian artery treated successfully with hybrid endovascular and open procedures in a patient with TS. Left carotid to subclavian artery bypass, thoracic endovascular aortic repair, and coil embolization of the aberrant right subclavian and left subclavian arteries were performed in an emergency setting. Literature on epidemiology, causes, and management options of acute aortic dissection in TS patients are reviewed and discussed.
特纳综合征（TS）已被证明是年轻女性主动脉夹层最常见的病因。然而，血管外科对这些患者关注甚少。我们报告了首例患有TS的患者，其B型主动脉夹层破裂并伴有迷走右锁骨下动脉，通过血管腔内和开放手术相结合的方式成功治疗。在紧急情况下进行了左颈动脉至锁骨下动脉旁路移植术、胸主动脉腔内修复术以及对迷走右锁骨下动脉和左锁骨下动脉进行弹簧圈栓塞。本文对TS患者急性主动脉夹层的流行病学、病因及治疗选择的文献进行了综述和讨论。
