Yoon Jong Hyung, Kim Hyery, Lee Ji Won, Kang Hyoung Jin, Park Hyeon Jin, Park Kyung Duk, Park Byung-Kiu, Shin Hee Young, Park June Dong, Park Sung-Hye, Ahn Hyo Seop
*Department of Pediatrics, Division of Hematology/Oncology, Cancer Research Institute ‡Department of Pathology, Seoul National University College of Medicine, Seoul †Center for Pediatric Oncology, National Cancer Center, Goyang, Korea.
J Pediatr Hematol Oncol. 2014 Oct;36(7):e456-9. doi: 10.1097/MPH.0000000000000058.
Ewing sarcoma/peripheral primitive neuroectodermal tumors (ES/pPNETs) typically occur in the long or flat bones, the chest wall, extraskeletal soft tissue, or less frequently, in solid organs. They can arise from anywhere in the body; however, ES/pPNETs arising from the adrenal gland are very rare, especially in children and adolescents. Herein, the authors report a case of an ES/pPNET in the adrenal gland of a 17-year-old girl, who was successfully treated with a multimodal treatment, with a brief review of the pertinent literature.
尤因肉瘤/外周原始神经外胚层肿瘤(ES/pPNETs)通常发生于长骨或扁骨、胸壁、骨骼外软组织,或较少见地发生于实体器官。它们可起源于身体的任何部位;然而,起源于肾上腺的ES/pPNETs非常罕见,尤其是在儿童和青少年中。在此,作者报告一例17岁女孩肾上腺ES/pPNETs病例,该病例通过多模式治疗成功治愈,并对相关文献进行简要回顾。