Department of Neurosurgery, RUSH University Medical Center, 1725 W Harrison Street, Suite 855, Chicago, IL 60612, USA.
Department of Neurosurgery, RUSH University Medical Center, 1725 W Harrison Street, Suite 855, Chicago, IL 60612, USA.
J Clin Neurosci. 2014 Jul;21(7):1254-6. doi: 10.1016/j.jocn.2013.11.003. Epub 2013 Nov 27.
Paget's disease is the second most common metabolic bone disease after osteoporosis and is characterized by abnormal bone turnover and remodeling that can lead to pain, pathological fracture, bony deformity and nerve compression syndromes. The lumbar region is the most commonly affected site within the spine followed by the thoracic and cervical spine. Even though the spine is affected very commonly in Paget's disease, malignant degeneration is exceptionally rare. Multilevel monostotic spine involvement due to Paget's disease is very uncommon. An unusual clinico-radiological manifestation of multilevel thoracic Paget's disease with sarcomatous degeneration presenting as a neurosurgical emergency is reported with a pertinent review of the literature.
佩吉特病是仅次于骨质疏松症的第二大常见代谢性骨病,其特征为异常的骨转换和重塑,可导致疼痛、病理性骨折、骨畸形和神经压迫综合征。脊柱中腰椎区是最常受累的部位,其次是胸椎和颈椎。尽管脊柱在佩吉特病中非常常见,但恶变极为罕见。由于佩吉特病引起的多节段单发性脊柱受累非常少见。本文报道了一例不常见的多节段胸段佩吉特病伴肉瘤样恶变的临床-影像学表现,其表现为神经外科急症,并进行了相关文献复习。